MS-2691

A 7-day-old infant is brought to a community paediatrician by a general physician due to poor feeding, vomiting, and increasing lethargy. The baby was born at term through a spontaneous vaginal delivery, and antenatal scans showed no complications.

During the examination, the infant appears weak and exhausted. The nappy is wet and has a distinct smell of maple syrup.

What is the potential complication of leaving this condition untreated, considering the most probable diagnosis?